Title: Personality profiles of children and adolescents with neurofibromatosis type 1
Authors: Prinzie, Peter ×
Descheemaeker, Mie-Jef
Vogels, Annick
Cleymans, T
Haselager, G J T
Curfs, L M G
Hellinckx, Walter
Onghena, Patrick
Legius, Eric
van Lieshout, C F M
Fryns, Jean-Pierre #
Issue Date: Apr-2003
Publisher: Wiley-Liss
Series Title: American Journal of Medical Genetics vol:118 issue:1 pages:1-7
Abstract: The personality profile of 44 youngsters (24 males, 20 females; mean age 11 years, 3 months) with neurofibromatosis type 1 (NF1) was compared with a group of 220 non-NF1 control youngsters (matched on age and gender). Personality characteristics of each youngster were rated by both parents, using the California Child Q-set (CCQ); [Block and Block, 1980]. The scores on eight personality dimensions were compared, i.e., Extraversion, Agreeableness, Conscientiousness, Emotional Stability, Openness, Motor Activity, Irritability, and Dependency. Moreover, personality of NF1 youngsters was related to IQ level, severity of medical problems, the presence or absence of visible cosmetic disfiguring, and de novo versus familial origin of NF1. The personality profile of NF1 youngsters was markedly different from the non-NF1 youngsters. Compared to the 220 control children, they were equally agreeable, but less conscientious, less emotionally stable, less open for new experience, with less motor activity, and more extravert, more dependent, and more irritable. Personality characteristics were similar for children with maternally or paternally inherited NF1, or for children with a new mutation. There was no association with gender, the severity of medical and cosmetic problems, and IQ.
Description: Centrum voor Orthopedagogiek. Departement Pedagogische wetenschappen. Afdeling Fundamentele en comparatieve pedagogiek en methodologie. Centrum voor Methodologie van het pedagogisch onderzoek. Leuvens Instituut voor onderwijsonderzoek (LIVO) Afdeling Centrum Menselijke erfelijkheid - UZ.
ISSN: 0148-7299
Publication status: published
KU Leuven publication type: IT
Appears in Collections:Parenting and Special Education
Methodology of Educational Sciences
Clinical Genetics Section (-)
Department of Human Genetics - miscellaneous
× corresponding author
# (joint) last author

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