Title: Personality profiles of youngsters with velo-cardio-facial syndrome
Authors: Prinzie, Peter ×
Swillen, Ann
Vogels, Annick
Kockuyt, V
Curfs, L
Haselager, G
Hellinckx, Walter
Devriendt, Koenraad
Onghena, Patrick
Van Lieshout, C F M
Fryns, Jean-Pierre #
Issue Date: Nov-2002
Publisher: Edition médicine et hygiène
Series Title: Genetic Counseling vol:13 issue:3 pages:265-80
Abstract: The personality profile of 48 youngsters (24 males and 24 females, mean age 8 years, 5 months) with Velo-Cardio-Facial Syndrome (VCFS) was compared with a group of 240 non VCFS control youngsters (matched on age and gender), and, in addition, with groups of youngsters with Prader-Willi (PWS), Fragile X (FXS), and Williams Syndromes (WS). Personality characteristics of each youngster were rated by both parents, using the California Child Q-set (CCQ). The scores on eight personality dimensions were compared, i.e., Extraversion, Agreeableness, Conscientiousness, Emotional Stability, Openness, Motor Activity, Irritability, and Dependency. Moreover, Individual differences in personality of VCFS youngsters were related to IQ level, presence or absence of cardiac defects, and de novo versus familial origin of VCFS. The personality profile of VCFS youngsters was markedly different from all non-VCFS groups. Compared to the 240 control children, they were equally extravert and agreeable, less conscientious and emotional stable and more Irritable and dependent. Some personality characteristics in youngsters with VCFS were related to IQ and Age, but not to cardiac defects or de novo versus familial genetic origin of the 22q11 deletion.
ISSN: 1015-8146
Publication status: published
KU Leuven publication type: IT
Appears in Collections:Clinical Genetics Section (-)
Parenting and Special Education
Methodology of Educational Sciences
Research Group for Adapted Physical Activity and Psychomotor Rehabilitation
Department of Human Genetics - miscellaneous
× corresponding author
# (joint) last author

Files in This Item:

There are no files associated with this item.

Request a copy


All items in Lirias are protected by copyright, with all rights reserved.

© Web of science