Clear cell sarcoma (CCS) is a rare soft tissue sarcoma that shows melanocytic differentiation and typically presents in the distal extremities of young adults. A subset of CCS also occurs within the gastrointestinal tract, including a histologic variant rich in osteoclast-type giant cells. Although these tumours are also S100 protein positive, they typically lack melanosomes and do not express other melanocytic markers such as HMB-45 and Melan-A. Therefore, these gastrointestinal tumours probably represent a distinct entity from the CCS of soft tissue. However, lesions of CCS occurring outside of these two settings are very rare.(1) The authors present a case of CCS which has not been previously reported as a primary lesion in an oral location. This article is protected by copyright. All rights reserved.