Title: Behavior of Ebstein's Anomaly: Single-Center Experience and Midterm Follow-Up
Authors: Legius, Barbara ×
Van De Bruaene, Alexander
Van Deyk, Kristien
Gewillig, Marc
Troost, Els
Meyns, Bart
Budts, Werner #
Issue Date: 2010
Publisher: Karger
Series Title: Cardiology vol:117 issue:2 pages:90-95
Abstract: Objectives: Ebstein's anomaly, characterized by an apical displacement of the tricuspid valve into the right ventricle, occurs in approximately 1/200,000 live births. Because long-term follow-up data of adults with Ebstein's anomaly are scarce, we evaluated the outcome of our Ebstein's anomaly patients. Methods: All patients >16 years and registered in the congenital heart disease database of our hospital with isolated Ebstein's anomaly were selected for the study. Records were reviewed for outcome. Results: Forty-nine patients (21 males, mean age at diagnosis 29.1 +/- 20.7 years) were followed for a mean time of 11.4 years (range 1.1-32.4). Twenty-five patients (51%) underwent tricuspid valve surgery (16 valvuloplasty and 9 valve replacement). Eight patients (32%) required redo tricuspid valve surgery. Twenty-six patients (52.1%) exhibited supraventricular arrhythmia, and the typical Wolff-Parkinson-White syndrome occurred in 15 patients (31.2%). Seventeen patients (34.7%) underwent ablation therapy and 5 patients (10.4%) required pacemaker implantation. Conclusions: Half of the patients with Ebstein's anomaly needed tricuspid valve surgery and redo surgery was not uncommon. Supraventricular arrhythmia occurred frequently and ablation therapy was often indicated. Careful follow-up is obligate, as some complications occur for the first time in adulthood. Copyright (C) 2010 S. Karger AG, Basel
ISSN: 0008-6312
Publication status: published
KU Leuven publication type: IT
Appears in Collections:Cardiology
Cardiac Surgery
Cardiovascular Developmental Biology
× corresponding author
# (joint) last author

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